Mauriac Syndrome: A Rare Hepatic Glycogenosis in Poorly Controlled Type 1 Diabetes

Background: Hepatic glycogenosis (HG) is a complication of poorly controlled type 1 diabetes mellitus (T1DM), characterized by glycogen accumulation in hepatocytes. Mauriac syndrome (MS) is a glycogenic hepatopathy, initially described in 1930, characterized by growth failure, delayed puberty, cushi...

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Bibliographic Details
Main Authors: Marta Patita, Gonçalo Nunes, António Alves de Matos, Hélder Coelho, Cristina Fonseca, Jorge Fonseca
Format: Article
Language:English
Published: Karger Publishers 2019-01-01
Series:GE: Portuguese Journal of Gastroenterology
Subjects:
Online Access:https://www.karger.com/Article/FullText/496094