Langerhans cell histiocytosis

The authors present a rare case of Langerhans cell histiocytosis in a 31 year old female patient with vulvar, peri-anal and oral lesions, diabetes insipidus, pulmonary skin and bone infiltrations. Skin biopsy immunohistochemistry presented positive S100 protein and vimentine, but the diagnosis was d...

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Bibliographic Details
Main Authors: Maria de Lourdes L. F. Chauffaille, Rosana M. Valério, Cybelle Maria Costa Diniz, Milvia Maria Simões, Silva Enokihara, Nylceo Michalany, Karin Ventura Ferreira, José Antonio Baddini Martinez, Karine Marques Hassun, Álvaro Nagib Atallah, José Kerbauy
Format: Article
Language:English
Published: Associação Paulista de Medicina
Series:São Paulo Medical Journal
Subjects:
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801998000100006&lng=en&tlng=en