The factors affecting lipid profile in adult patients with Mucopolysaccharidosis

Background: Mucopolysaccharidoses (MPS) are a group of rare inherited disorders characterized by abnormal accumulation of glycosaminoglycans (GAGs) within the myocytes and coronary arteries. Little is known about hyperlipidaemia as a potential cardiovascular risk factor in these patients. Baseline c...

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Bibliographic Details
Main Authors: Karolina M. Stepien, Fiona J. Stewart, Chris J. Hendriksz
Format: Article
Language:English
Published: Elsevier 2017-09-01
Series:Molecular Genetics and Metabolism Reports
Subjects:
MPS
BMI
Online Access:http://www.sciencedirect.com/science/article/pii/S2214426917300381