Pachyonychia Congenita type 1 – A peerless entity

Pachyonychia congenita (PC) is a rare Autosomal dominant genodermatosis characterized by hyperkeratosis affecting the nails and palmoplantar areas, oral leucokeratosis, and cystic lesions. Although classically subdivided into two major variants, PC-1 (Jadassohn-Lewandowski syndrome) and PC-2 (Jackso...

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Bibliographic Details
Main Authors: Yugandar Inakanti, Venkata Narsimha Rao Thimmasarthi, Shiva Kumar, Akshaya Nagaraj, Srilakshmi Peddireddy
Format: Article
Language:English
Published: Our Dermatology Online 2015-07-01
Series:Nasza Dermatologia Online
Subjects:
Online Access:http://www.odermatol.com/issue-in-html/2015-3-22/