Biochemical studies on the physiopathology of MCAD, LCHAD and MTP deficiencies in human fibroblasts and rodent tissues : evidence of disruption of redox and energy homeostasis by accumulated metabolites

Biochemical studies on the physiopathology of MCAD, LCHAD and MTP deficiencies in human fibroblasts and rodent tissues : evidence of disruption of redox and energy homeostasis by accumulated metabolites

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A deficiência da desidrogenase de acilas-CoA de cadeia média (MCAD) é um defeito da oxidação de ácidos graxos (DOAG) bioquimicamente caracterizada pelo acúmulo de acilcarnitinas de cadeia média (MCAC) em tecidos e líquidos biológicos de indivíduos afetados. Clinicamente os pacientes apresentam sinto...

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Bibliographic Details
Main Author: Tonin, Anelise Miotti
Other Authors: Wajner, Moacir
Format: Others
Language:English
Published: 2014
Subjects:
Estresse oxidativo
Ácidos graxos
Oxidação
Acil-CoA desidrogenase
3-hidroxiacil-CoA desidrogenase de cadeia longa
Homeostase
Fibroblastos
Online Access:http://hdl.handle.net/10183/94887

Internet

http://hdl.handle.net/10183/94887

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