Urinary Transthyretin as a Biomarker in ATTRv Val50Met Amyloidosis

Transthyretin (TTR), the precursor protein for amyloidogenic TTR (ATTR) amyloidosis, forms tetramers and escapes glomerular filtration by binding with thyroxine and retinol-binding protein. However, variant TTRs are unstable as tetramers, so monomeric TTR has become the precursor protein of amyloid...

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Bibliographic Details
Main Authors: Ando, Y. (Author), Inoue, F. (Author), Masuda, T. (Author), Matsushita, H. (Author), Misumi, Y. (Author), Okada, M. (Author), Ueda, M. (Author)
Format: Article
Language:English
Published: MDPI 2022
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