Neutrophils from Patients with Primary Ciliary Dyskinesia Display Reduced Chemotaxis to CXCR2 Ligands

by Maaike Cockx, Mieke Gouwy, Véronique Godding, Kris De Boeck, Jo Van Damme, Mieke Boon, Sofie Struyf
Published 2017-09-01

The Antimicrobial Activity of Peripheral Blood Neutrophils Is Altered in Patients with Primary Ciliary Dyskinesia

by Maaike Cockx, Marfa Blanter, Mieke Gouwy, Pieter Ruytinx, Sara Abouelasrar Salama, Sofie Knoops, Noëmie Pörtner, Lotte Vanbrabant, Natalie Lorent, Mieke Boon, Sofie Struyf
Published 2021-06-01

Optimisation of children z-score calculation based on new statistical techniques.

by Antonio Martinez-Millana, Jessie M Hulst, Mieke Boon, Peter Witters, Carlos Fernandez-Llatas, Ines Asseiceira, Joaquin Calvo-Lerma, Ignacio Basagoiti, Vicente Traver, Kris De Boeck, Carmen Ribes-Koninckx
Published 2018-01-01

Change in Nutrient and Dietary Intake in European Children with Cystic Fibrosis after a 6-Month Intervention with a Self-Management mHealth Tool

by Joaquim Calvo-Lerma, Mieke Boon, Jessie Hulst, Carla Colombo, Inês Asseiceira, María Garriga, Etna Masip, Ine Claes, Anna Bulfamante, Hettie M. Janssens, Maria Roca, Saioa Vicente, Victoria Fornés, Laura Zazzeron, Bo van Schijndel, Sandra Woodcock, Luisa Pereira, Kris de Boeck, Carmen Ribes-Koninckx
Published 2021-05-01

Clinical validation of an evidence-based method to adjust Pancreatic Enzyme Replacement Therapy through a prospective interventional study in paediatric patients with Cystic Fibros...

by Joaquim Calvo-Lerma, Jessie Hulst, Mieke Boon, Carla Colombo, Etna Masip, Mar Ruperto, Victoria Fornés-Ferrer, Els van der Wiel, Ine Claes, Maria Garriga, Maria Roca, Paula Crespo-Escobar, Anna Bulfamante, Sandra Woodcock, Sandra Martínez-Barona, Ana Andrés, Kris de Boeck, Carmen Ribes-Koninckx, MyCyFAPP project
Published 2019-01-01

Access to medicines for rare diseases: beating the drum for primary ciliary dyskinesia

by Suzanne Crowley, Inês Azevedo, Mieke Boon, Andrew Bush, Ernst Eber, Eric Haarman, Bulent Karadag, Karsten Kötz, Margaret Leigh, Antonio Moreno-Galdó, Huda Mussaffi, Kim G. Nielsen, Heymut Omran, Jean-François Papon, Petr Pohunek, Kostas Priftis, Bernhard Rindlisbacher, Francesca Santamaria, Arunas Valiulis, Michal Witt, Panayiotis Yiallouros, Zorica Zivkovic, Claudia E. Kuehni, Jane S. Lucas
Published 2020-09-01

Standardised clinical data from patients with primary ciliary dyskinesia: FOLLOW-PCD

by Myrofora Goutaki, Jean-François Papon, Mieke Boon, Carmen Casaulta, Ernst Eber, Estelle Escudier, Florian S. Halbeisen, Amanda Harris, Claire Hogg, Isabelle Honore, Andreas Jung, Bulent Karadag, Cordula Koerner-Rettberg, Marie Legendre, Bernard Maitre, Kim G. Nielsen, Bruna Rubbo, Nisreen Rumman, Lynne Schofield, Amelia Shoemark, Guillaume Thouvenin, Hannah Willkins, Jane S. Lucas, Claudia E. Kuehni
Published 2020-02-01

International BEAT-PCD consensus statement for infection prevention and control for primary ciliary dyskinesia in collaboration with ERN-LUNG PCD Core Network and patient represent...

by June K. Marthin, Jane S. Lucas, Mieke Boon, Carmen Casaulta, Suzanne Crowley, Damien M.S. Destouches, Ernst Eber, Amparo Escribano, Eric Haarman, Claire Hogg, Bernard Maitre, Gemma Marsh, Vendula Martinu, Antonio Moreno-Galdó, Huda Mussaffi, Heymut Omran, Petr Pohunek, Bernhard Rindlisbacher, Phil Robinson, Deborah Snijders, Woolf T. Walker, Panayiotis Yiallouros, Helle Krogh Johansen, Kim G. Nielsen
Published 2021-08-01

Assessing gastro-intestinal related quality of life in cystic fibrosis: Validation of PedsQL GI in children and their parents.

by Mieke Boon, Ine Claes, Trudy Havermans, Victoria Fornés-Ferrer, Joaquim Calvo-Lerma, Inês Asseiceira, Anna Bulfamante, María Garriga, Etna Masip, Sandra Woodcock, Sylvia Walet, Celeste Barreto, Carla Colombo, Paula Crespo, Els Van der Wiel, Jessie Hulst, Sandra Martinez-Barona, Rita Nobili, Luisa Pereira, Mar Ruperto, Saioa Vicente, Kris De Boeck, Carmen Ribes-Koninckx, MyCyFAPP consortium
Published 2019-01-01

Pulmonary exacerbations in patients with primary ciliary dyskinesia: an expert consensus definition for use in clinical trials

by Jane S. Lucas, Florian Gahleitner, Adelina Amorim, Mieke Boon, Philippa Brown, Carolina Constant, Simon Cook, Suzanne Crowley, Damien M.S. Destouches, Ernst Eber, Huda Mussaffi, Eric Haarman, Amanda Harris, Cordula Koerner-Rettberg, Claudia E. Kuehni, Philipp Latzin, Michael R. Loebinger, Natalie Lorent, Bernard Maitre, Antonio Moreno-Galdó, Kim G. Nielsen, Uğur Özçelik, Lue Katrine Drasbæk Philipsen, Petr Pohunek, Eva Polverino, Jessica Rademacher, Phil Robinson, Deborah Snijders, Panayiotis Yiallouros, Siobhán B. Carr
Published 2019-02-01

Prevalence and course of disease after lung resection in primary ciliary dyskinesia: a cohort & nested case-control study

by Panayiotis Kouis, Myrofora Goutaki, Florian S. Halbeisen, Ifigeneia Gioti, Nicos Middleton, Israel Amirav, on behalf of the Israeli PCD Consortium, Angelo Barbato, on behalf of the Italian PCD Consortium, Laura Behan, Mieke Boon, Nagehan Emiralioglu, Eric G. Haarman, Bulent Karadag, Cordula Koerner-Rettberg, Romain Lazor, on behalf of the Swiss PCD Group, Michael R. Loebinger, Bernard Maitre, on behalf of the French Reference Centre for Rare Lung Diseases, Henryk Mazurek, Lucy Morgan, Kim Gjerum Nielsen, Heymut Omran, Ugur Özçelik, Mareike Price, Andrzej Pogorzelski, Deborah Snijders, on behalf of the PCD Italian Consortium, Guillaume Thouvenin, on behalf of the French Reference Centre for Rare Lung Diseases, Claudius Werner, Zorica Zivkovic, Claudia E. Kuehni, Panayiotis K. Yiallouros
Published 2019-09-01