Continuous use of glycomacropeptide in the nutritional management of patients with phenylketonuria: a clinical perspective

Continuous use of glycomacropeptide in the nutritional management of patients with phenylketonuria: a clinical perspective

Abstract Background In phenylketonuria (PKU), modified casein glycomacropeptide supplements (CGMP-AA) are used as an alternative to the traditional phenylalanine (Phe)-free L-amino acid supplements (L-AA). However, studies focusing on the long-term nutritional status of CGMP-AA are lacking. This ret...

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Bibliographic Details
Main Authors: Maria João Pena, Alex Pinto, Manuela Ferreira de Almeida, Catarina de Sousa Barbosa, Paula Cristina Ramos, Sara Rocha, Arlindo Guimas, Rosa Ribeiro, Esmeralda Martins, Anabela Bandeira, Cláudia Camila Dias, Anita MacDonald, Nuno Borges, Júlio César Rocha
Format: Article
Language:English
Published: BMC 2021-02-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Casein glycomacropeptide
Amino acids
Nutritional status
Phenylketonuria
Phenylalanine
Tyrosine
Online Access:https://doi.org/10.1186/s13023-021-01721-8

Internet

https://doi.org/10.1186/s13023-021-01721-8

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