Over Restriction of Dietary Protein Allowance: The Importance of Ongoing Reassessment of Natural Protein Tolerance in Phenylketonuria

Over Restriction of Dietary Protein Allowance: The Importance of Ongoing Reassessment of Natural Protein Tolerance in Phenylketonuria

Phenylalanine (Phe) tolerance is highly variable in phenylketonuria (PKU) and rarely described in patients aged ≥12 years. Patients ≥12 years of age with PKU were systematically challenged with additional natural protein (NP) if blood Phe levels remained below 480 µmol/L (i.e., upper target blood Ph...

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Bibliographic Details
Main Authors: Alex Pinto, Manuela Ferreira Almeida, Anita MacDonald, Paula Cristina Ramos, Sara Rocha, Arlindo Guimas, Rosa Ribeiro, Esmeralda Martins, Anabela Bandeira, Richard Jackson, Francjan van Spronsen, Anne Payne, Júlio César Rocha
Format: Article
Language:English
Published: MDPI AG 2019-04-01
Series:Nutrients
Subjects:
BH4
natural protein tolerance
phenylketonuria
phenylalanine
Online Access:https://www.mdpi.com/2072-6643/11/5/995

Internet

https://www.mdpi.com/2072-6643/11/5/995

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